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Related papers: Cerebellar Purkinje Cell Loss in Heterozygous Rora…

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Homozygous mutations in the progranulin gene (GRN) are associated with neuronal ceroid lipofuscinosis 11 (CLN11), a rare lysosomal-storage disorder characterized by cerebellar ataxia, seizures, retinitis pigmentosa, and cognitive disorders,…

Simple spike synchrony between Purkinje cells projecting to a common neuron in the deep cerebellar nucleus is emerging as an important factor in the encoding of output information from cerebellar cortex. Stochastic synchronization is a…

Neurons and Cognition · Quantitative Biology 2014-08-14 Sergio Verduzco-Flores

Several experiments and models have highlighted the importance of neuronal heterogeneity in brain dynamics and function. However, how such a cell-to-cell diversity can affect cortical computation, synchronization, and neuronal communication…

Neurons and Cognition · Quantitative Biology 2021-04-07 Katiele V. P. Brito , Fernanda Selingardi Matias

Despite the popularity of homogeneous GPU-based deep learning (DL) training, the prevalence, causes and impact of stragglers and the effectiveness of existing straggler mitigation approaches are still not well understood in this scenario…

Distributed, Parallel, and Cluster Computing · Computer Science 2025-12-11 Zeyu Zhang , Haiying Shen

Transforming growth factor beta (TGF$\beta$) plays a central role in morphogenesis, growth, and cell differentiation. This cytokine is particularly important in cartilage where it regulates cell proliferation and extracellular matrix…

Tissues and Organs · Quantitative Biology 2015-05-27 Catherine Baugé , Olivier Cauvard , Sylvain Leclercq , Philippe Galéra , Karim Boumédiene

The effect of histamine (HA) on the electric activities of Purkinje cell (PC) is studied on the cerebellum slice. We find that: (1) HA's main effect on PC is excitative (72.9%); there are also a small amount of PC showing inhibitive (10.2%)…

Biological Physics · Physics 2007-05-23 Lin Tang

Supervised learning has long been attributed to several feed-forward neural circuits within the brain, with attention being paid to the cerebellar granular layer. The focus of this study is to evaluate the input activity representation of…

Neural and Evolutionary Computing · Computer Science 2020-03-04 Richard R Carrillo , Francisco Naveros , Eduardo Ros , Niceto R Luque

The cerebellar Purkinje cell controlling eyeblinks can learn, remember and reproduce the interstimulus interval in a classical conditioning paradigm. Given temporally separated inputs, the cerebellar Purkinje cell learns to pause its tonic…

Neurons and Cognition · Quantitative Biology 2016-05-13 Matthew Ricci , Junkyung Kim , Fredrik Johansson

A variety of missense mutations and a stop mutation in the gene coding for transmembrane protein 240 (TMEM240) have been reported to be the causative mutations of spinocerebellar ataxia 21 (SCA21). We aimed to investigate the expression of…

The brain as a neuronal system has very complex structure with large diversity of neuronal types. The most basic complexity is seen from the structure of neuronal morphology, which usually has a complex tree-like structure with dendritic…

Neurons and Cognition · Quantitative Biology 2019-05-08 Lingling An , Yuanhong Tang , Quan Wang , Qingqi Pei , Ran Wei , Huiyuan Duan , Jian K. Liu

Electrophysiological recordings of neural activity in a mouse's brain are very popular among neuroscientists for understanding brain function. One particular area of interest is acquiring recordings from the Purkinje cells in the cerebellum…

Individual brains exhibit striking structural and physiological heterogeneity, yet neural circuits can generate remarkably consistent functional properties across individuals, an apparent paradox in neuroscience. While recent studies have…

Neurons and Cognition · Quantitative Biology 2025-05-08 Yu Zhu , Chunfeng Song , Wanli Ouyang , Shan Yu , Tiejun Huang

The aim of this study was to estimate the number of new cells and neurons added to the dentate gyrus across the lifespan, and to compare the rate of age-associated decline in neurogenesis across species. Data from mice (Mus musculus), rats…

Neurons and Cognition · Quantitative Biology 2011-05-05 Stanley E. Lazic

Cerebellum is part of the brain that occupies only 10% of the brain volume, but it contains about 80% of total number of brain neurons. New cerebellar function model is developed that sets cerebellar circuits in context of multibody…

Neural and Evolutionary Computing · Computer Science 2014-02-25 Lavdim Kurtaj , Ilir Limani , Vjosa Shatri , Avni Skeja

We consider a cerebellar ring network for the optokinetic response (OKR), and investigate the effect of diverse recoding of granule (GR) cells on OKR by varying the connection probability $p_c$ from Golgi to GR cells. For an optimal value…

Neurons and Cognition · Quantitative Biology 2020-08-12 Sang-Yoon Kim , Woochang Lim

Retinoic acid receptor (RAR) is a ligand-dependent transcription factor that regulates the expression of genes involved in cell growth, differentiation, and development. Binding of the retinoic acid hormone to RAR is accompanied by…

Biological Physics · Physics 2009-10-31 Dorina Kosztin , Sergei Izrailev , Klaus Schulten

For long it has been known that specific patterns of folding are necessary for an optimally functioning brain. For instance, lissencephaly and polymicrogyria can lead to severe mental retardation, short life expectancy, epileptic seizures,…

Biological Physics · Physics 2020-04-03 Lucas da Costa Campos , Raphael Hornung , Gerhard Gompper , Jens Elgeti , Svenja Caspers

A toggle switch consists of two genes that mutually repress each other. This regulatory motif is active during cell differentiation and is thought to act as a memory device, being able to choose and maintain cell fate decisions. In this…

Molecular Networks · Quantitative Biology 2018-12-26 Michael K. Strasser , Fabian J. Theis , Carsten Marr

A curious feature of organ and organoid morphogenesis is that in certain cases, spatial oscillations in the thickness of the growing "film" are out-of-phase with the deformation of the slower-growing "substrate," while in other cases, the…

Biological Physics · Physics 2018-12-26 T. A. Engstrom , Teng Zhang , A. K. Lawton , A. L. Joyner , J. M. Schwarz

BACKGROUND: Spinocerebellar ataxia types 19 and 22 (SCA19/22) are rare conditions in which relatively isolated cerebellar involvement is frequently associated with cognitive impairment. Here, we report on new clinical features and provide…

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